{{Rsnum
|rsid=199476117
|Chromosome=MT
|Orientation=plus
|geno1=(C;C)
|geno2=(C;T)
|geno3=(T;T)
|Gene=SESN3
|position=10158
|Assembly=GRCh38
|GenomeBuild=38.1
|dbSNPBuild=141
|Gene_s=MT-CO3
}}{{ClinVar
|ALT=C
|CHROM=MT
|CLNACC=RCV000010360.1; RCV000010361.1
|CLNALLE=1
|CLNDBN=Leigh syndrome due to mitochondrial complex I deficiency; Mitochondrial complex I deficiency
|CLNDSDB=MedGen; MedGen:OMIM
|CLNDSDBID=C1838951; C1838979:252010
|CLNHGVS=NC_012920.1:m.10158T>C
|CLNSIG=5
|CLNSRC=OMIM Allelic Variant
|CLNSRCID=516002.0003
|Disease=Leigh syndrome due to mitochondrial complex I deficiency; Mitochondrial complex I deficiency
|FwdALT=C
|FwdREF=T
|REF=T
|RSPOS=10158
|Reversed=0
|SAO=0
|SSR=0
|Tags=PM;OTHERKG;LSD;OM
|VC=SNV
|VP=0x050060000000000002110100
|WGT=0
|dbSNPBuildID=136
|rsid=199476117
}}